大疱性系统性红斑狼疮

Gammon等提出本病的诊断要点为:i①符合SLE的诊断标准;②获得性非瘢痕性大疱;③表皮下大疱,l真皮上和基底膜带以中性粒细胞为主的炎症浸润;④直接免疫荧光(DIF)检查示皮损及周围皮肤有IgG或伴有IgM和IgA沉积。免疫电镜(IEM)检查可见免疫球蛋白沉积于致密板和致密板下区。

引自:i

Gammon1WR,lRriggaman1RA.Bullous1SLE:iA1phenotypically1distinctive1but1immunologically1heterogeneous1bullous1disorder[J].J1Invest1Dermatol,l1993,l100(1):i28S~34S.